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Dernières publications
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Julia Pereira Lemos, Liliane Patrícia Gonçalves Tenório, Vincent Mouly, Gillian Butler-Browne, Daniella Arêas Mendes-Da-Cruz, et al.. T cell biology in neuromuscular disorders: a focus on Duchenne Muscular Dystrophy and Amyotrophic Lateral Sclerosis. Frontiers in Immunology, 2023, 14, pp.120283. ⟨10.3389/fimmu.2023.1202834⟩. ⟨hal-04603915⟩
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Fanny Roth, Jamila Dhiab, Alexis Boulinguiez, Hadidja-Rose Mouigni, Saskia Lassche, et al.. Assessment of PABPN1 nuclear inclusions on a large cohort of patients and in a human xenograft model of oculopharyngeal muscular dystrophy. Acta Neuropathologica, 2022, ⟨10.1007/s00401-022-02503-7⟩. ⟨hal-03832636⟩
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Elisa Negroni, Maria Kondili, Laura Muraine, Mona Bensalah, Gillian Sandra Butler-Browne, et al.. Muscle fibro-adipogenic progenitors from a single-cell perspective: Focus on their “virtual” secretome. Frontiers in Cell and Developmental Biology, 2022, 10, ⟨10.3389/fcell.2022.952041⟩. ⟨hal-03830589⟩
Chiffres clés
103
Publications avec texte intégral
Open Access
60 %
Mots clés
Metabolism
Mass spectrometry
Ageing
Geriatric assessment
APOPTOSIS
Aged
Nuclear envelope
Lamins
Triplet expansion disease
Neuromuscular junction NMJ
Myotube
OPMD
Autologous
Muscle fibrosis
PABPN1
Muscle
Differentiation
Epigenetics
Haploinsufficiency
Myosin
Dystrophie musculaire oculopharyngée
Aggregate
Myopathy
FAPs
Atrophy
Sarcopenia
AAV vectors
Muscle strength
Thérapie génique
Transcriptomics
Actin
Neuromuscular disease
ALS
Regulatory T cells
Accelerometry
Omics
Intercellular communication
Amyotrophic Lateral Sclerosis
DMD
Fibrosis
Annexin A2
Myoblasts
2-D PAGE
Myogenesis
Cross-bridge kinetics
Regeneration
Antisens oligonucleotides
Calcium
Alphavirus
Myoblast
Anti-fibrotic pharmacotherapies
BINDING SPECIFICITY
Dysferlinopathy
Arbovirus
DUX4
GENE
Myopathies
AAV
Functional genomics
MUTATIONS
Satellite cell
Andermann syndrome
Myositis
Regenerative medicine
Dystrophin
Oculopharyngeal muscular dystrophy
Dysferlin
PABPN1 agregates
DNA methylation
Pax7
Anti-acetylcholine receptor antibodies
Gene replacement
AChR antibodies
Effector T cells
Bile salt hydrolases
Alzheimer's disease
Autoimmune diseases
Human
Biomarker
Agrégats de PABPN1
Satellite cells
Muscle stem cells
AUTOPHAGY
Aav-U7
Adipose tissue
Gene therapy
Exon-skipping
Muscle dystrophy
Akt
Muscular dystrophy
Cell therapy
Antiserum
FSHD
RNA
Inflammation
Pharyngeal muscle
Xenograft
Duchenne muscular dystrophy
ARN
Skeletal muscle